Response rates and survival in primary systemic amyloidosis
نویسندگان
چکیده
منابع مشابه
Response rates and survival in primary systemic amyloidosis.
Patients (153) with biopsy-proven primary systemic amyloidosis (AL) were evaluated for their response rate to alkylating agent-based chemotherapy. Twenty-seven of the patients (18%) responded. The serum creatinine concentration had an adverse effect on response rate (P = .05). In patients with nephrotic syndrome, a normal serum creatinine value, and no echocardiographic evidence of cardiac amyl...
متن کاملA case of primary systemic amyloidosis with nail dystrophy
We hereby report a 79-year-old Iranian man presenting with nail dystrophy and subsequent development of purpuric and ecchymotic plaques, hemorrhagic bullae, and infiltrated papules on the head, neck and trunk. Histological examination of the gingiva, bone marrow aspiration, and biopsy confirmed the diagnosis of primary systemic amyloidosis. In this case, nail dystrophy was the presenting sign o...
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Primary systemic amyloidosis is a rare entity. We report a case of primary systemic amyloidosis without any associated hematological abnormality who presented with macroglossia and hemorrhagic lesions around eyes and sub mammary region. There were soft lobulated masses around perianal region, labia majora and on external auditory meatus obstructing auditory canal. She was also operated for carp...
متن کاملPrimary Systemic Amyloidosis
, Pr. Harrold: This man was 68 when he died. He was a gentlemen's outfitter. Before illness he had had two hernia repairs, and during the 1914-1918 war he had had afew injuries to the arms and legs. He had also had a brief episode of jaundice. His final illness began in the summer of 1962. He died in the summer of 1963. In J962 he noticed the onset of progressive mild exertional dyspnoea. In No...
متن کاملPrimary Systemic Amyloidosis
We report here a case of a 35-year-old male who presented with multi-system disease, which on evaluation was found to be due to primary systemic amyloidosis. We present the myriad manifestations of this uncommon disease entity.
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ژورنال
عنوان ژورنال: Blood
سال: 1991
ISSN: 0006-4971,1528-0020
DOI: 10.1182/blood.v77.2.257.257